Table 2

Improvement in PAP in patients with sarcoidosis-associated pulmonary hypertension following bosentan treatment

Patient
Initial mean PAP (mmHg)
Follow-up mean PAP (mmHg)
Pulmonary hypertension therapy
Other sarcoidosis medications

1
73
41
Epoprostenol
Prednisone, methotrexate, azathioprine, infliximab
2a
63
45
Bosentan
Prednisone
3a
61
ND
Bosentan, epoprostenol
Prednisone, azathioprine
4
53
23
Amlodipine
Prednisone, methotrexate
5
50
ND
Bosentan
Prednisone, methotrexate
6
38
36
Bosentan
Prednisone, methotrexate, azathioprine
7
36
24
Bosentan
Prednisone, methotrexate, infliximab

Shown are data demonstrating improvement in pulmonary artery pressure (PAP) following addition of bosentan to standard anti-inflammatory therapy in a small cohort of patients with sarcoidosis-associated pulmonary hypertension. aPatient died. ND, not determined.

Baughman Arthritis Research & Therapy 2007 9(Suppl 2):S8   doi:10.1186/ar2192