Table 1

Attenuation of key pathways in systemic sclerosis: agents for evaluation

Candidate therapy
Target pathway

Bosentan
ETA/ETB pathway
Imatinib
PDGF receptor signalling
signalling Infliximab
TNF-α
Adalimumab
TNF-α
Etanercept
TNF-α
CAT-192
TGF-β1
GC-1008
TGF-β1, TGF-β2, TGF-β3
FG-3019
CTGF ligand
Alefacept
LFA3/CD2
Basiliximab
IL-2Rα
MLM-1202
CCR2
Efalizumab
LFA/ICAM-1

CCR, CC chemokine receptor; ETA/B, endothelin receptor subtype A/B; CTGF, connective tissue growth factor; ICAM, intercellular adhesion molecule; IL-2Rα, interleukin-2 receptor α; LFA, lymphocyte function associated; PDGF, platelet-derived growth factor; TGF, transforming growth factor; TNF, tumour necrosis factor.

Denton Arthritis Research & Therapy 2007 9(Suppl 2):S6   doi:10.1186/ar2190