Table 1

Classification of neutropenia

Type of neutropenia
Neutropenias

Congenital
Severe infantile agranulocytosis (Kostmann's syndrome)

Shwachman–Diamond–Oski syndrome

Myelokathexis/neutropenia with tetraploid nuclei

Cyclic neutropenia

Chediak–Higashi syndrome

Reticular dysgenesis

Dyskeratosis congenita


Acquired
Postinfectious neutropenia

Drug-induced neutropenia

Complement activation (haemodialysis, leukapheresis, ARDS)

Immune neutropenia

     Isoimmune neonatal neutropenia

     Alloimmune neutropenia (transfusion reaction)

     Autoimmune neutropenia – primary

          Benign of childhood

          Adult chronic form

     Autoimmune neutropenia – secondary

          Autoimmune diseases

          Large granular lymphocyte

          Other (see Table 3)

     Pure white cell aplasia

Chronic idiopathic neutropenia

Hypersplenism

Nutritional deficiency (vitamin B12 or folate deficiency)

Diseases affecting the bone marrow

     Postchemotherapy

     Aplastic anaemia

     Fanconi anaemia

     Myelodysplastic syndrome

     Acute and chronic leukaemia

ARDS, acute respiratory distress syndrome.

Capsoni et al. Arthritis Research & Therapy 2005 7:208   doi:10.1186/ar1803