Table 2 |
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Characteristic histopathologic patterns and radiologic findings in the interstitium of IPF and connective tissue-associated ILD |
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Disease association |
Characteristic histopathologic pattern |
Characteristic radiographic findings on HRCT |
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|
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Idiopathic pulmonary fibrosis |
Usual interstitial pneumonia |
Peripheral and bibasilar reticulonodular opacities with honeycombing |
|
Systemic sclerosis |
Nonspecific interstitial pneumonia |
Increased reticular markings, ground glass opacification, basilar prominence |
|
Usual interstitial pneumonia |
Peripheral and bibasilar reticulonodular opacities with honeycombing |
|
|
Rheumatoid arthritis |
Usual interstitial pneumonia |
Reticular changes and honeycombing |
|
Nonspecific interstitial pneumonia |
Ground-glass opacities with basilar prominence |
|
|
Polymyositis/dermatomyositis |
Nonspecific interstitial pneumonia |
As above |
|
Usual interstitial pneumonia |
As above |
|
|
Cryptogenic organizing pneumonia |
Patchy airspace consolidation, ground glass opacities |
|
|
Diffuse alveolar damage |
Diffuse ground glass opacities |
|
|
Sjögren's syndrome |
Nonspecific interstitial pneumonia |
As above |
|
Lymphocytic interstitial pneumonia |
Thin walled cysts, ground glass opacities, centrilobular nodules |
|
|
Systemic lupus erythematosus |
Acute interstitial pneumonia |
Ground glass opacities |
|
Mixed connective tissue disease |
Nonspecific interstitial pneumonia |
Septal thickening and ground glass opacities |
|
|
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HRCT, high-resolution computed tomography; ILD, interstitial lung disease; IPF, idiopathic pulmonary fibrosis. |
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Castelino and Varga Arthritis Research & Therapy 2010 12:213 doi:10.1186/ar3097 |
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